Variables | Frequency (%)/mean ± SD | |
---|---|---|
Age of onset (years) | 42.4 ± 15.4 | |
Disease duration (years) | 1.8 ± 1.4 | |
ALS-FRS scale | 37.2 ± 8.4 | |
Disease stagea | 1 | 11 (42.3%) |
2 | 11 (42.3%) | |
3 | 4 (15.4%) | |
Clinical phenotype | Bulbar | 2 (6.7%) |
Classic | 19 (63.3%) | |
Classic/familial | 7 (23.3%) | |
Flail chest | 1 (3.3%) | |
Local segment | 1 (3.3%) |